Matches in SemOpenAlex for { <https://semopenalex.org/work/W4367046911> ?p ?o ?g. }
- W4367046911 endingPage "S82" @default.
- W4367046911 startingPage "S66" @default.
- W4367046911 abstract "Mycosis fungoides (MF) and Sézary syndrome (SS) are a distinct disease entity of cutaneous T-cell lymphoma with heterogenous clinical features and prognosis. MF mainly involves skin and usually shows an indolent and favorable clinical course. In patients with advanced-stage disease, extracutaneous involvement including lymph nodes, viscera, and blood, or large cell transformation may be observed. SS is a leukemic form of advanced-stage MF, characterized by generalized erythroderma. Early-stage MF can be treated with skin-directed therapy. However, patients with refractory or advanced-stage disease are associated with severe symptoms or poor prognosis, requiring systemic therapy. Recent progress in understanding the pathogenesis of MF/SS has contributed to advances in the management of these rare diseases. This review aims to describe the clinical manifestations, diagnosis, risk stratification, and treatment strategy of MF/SS, focusing on the recent updates in the management of these diseases." @default.
- W4367046911 created "2023-04-27" @default.
- W4367046911 creator A5002662971 @default.
- W4367046911 date "2023-04-30" @default.
- W4367046911 modified "2023-09-30" @default.
- W4367046911 title "Mycosis fungoides and Sézary syndrome" @default.
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