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- W4386656375 endingPage "295" @default.
- W4386656375 startingPage "273" @default.
- W4386656375 abstract "Connective tissue diseases (CTDs) are characterized by disorders that affect extracellular matrix components resulting in abnormal remodeling, degeneration, and various tissue integrity. Some types of CTDs particularly affect the extracellular matrix structures in the vessels and cause reduced elasticity and strength of the vessel wall. Around 20% of all thoracic aortic diseases are associated with heritable CTDs, which is considered the second-highest risk factor for aortic dissection after hypertension. Aortic disease in patients with CTDs is often more extensive than those without CTDs. The disease can affect the entire aorta from the aortic root to the abdominal aorta and extend the peripheral vascular system. It may also involve other cardiovascular structures such as the mitral valve, seen in the Marfan syndrome. Thus complications of cardiovascular degenerations are the leading cause of mortality in patients with CTDs. The spectrum of the presentation includes aneurysms and dissections, especially in the thoracic aortic segment. These syndromes have an earlier onset and dilatation severity than degenerative disease. Half the patients who present with aortic catastrophes at a younger age, less than 50 years old, are diagnosed with CTD. This chapter aims to review the current information about aneurysmatic degeneration of CTDs, summarizing the evidence in diagnosis, current management, open surgical repair, endovascular repair, and surveillance." @default.
- W4386656375 created "2023-09-13" @default.
- W4386656375 creator A5037073947 @default.
- W4386656375 creator A5043875322 @default.
- W4386656375 creator A5069960433 @default.
- W4386656375 creator A5072821254 @default.
- W4386656375 date "2022-01-01" @default.
- W4386656375 modified "2023-10-18" @default.
- W4386656375 title "Aneurysmatic degeneration of connective tissue diseases: from diagnosis to treatment" @default.
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