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- W4387110111 endingPage "538" @default.
- W4387110111 startingPage "523" @default.
- W4387110111 abstract "Essential thrombocythemia (ET), one of the BCR-ABL-negative myeloproliferative neoplasms (MPNs), is a hematopoietic malignancy characterized by overproduction of platelets due to clonal expansion of megakaryocytes. Enhanced constitutive JAK-STAT (janus kinase 2—signal transducer and activator of transcription) signaling is central to disease pathophysiology. ET, presenting with persistent thrombocytosis, may represent a myriad of conditions and careful establishing of an accurate diagnosis is key to subsequent optimal management. This chapter reviews in detail goals of therapy in ET and treatment strategies incorporating cytoreductive, noncytoreductive, and novel therapies. Finally, approaches to specific scenarios and their management are discussed including young patients, triple-negative for classical driver mutation ET patients, pregnancy, and splanchnic vein thrombosis." @default.
- W4387110111 created "2023-09-28" @default.
- W4387110111 creator A5003941928 @default.
- W4387110111 creator A5046827092 @default.
- W4387110111 creator A5065093182 @default.
- W4387110111 date "2023-01-01" @default.
- W4387110111 modified "2023-10-13" @default.
- W4387110111 title "Treatment Algorithm of Essential Thrombocythemia" @default.
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