Matches in SemOpenAlex for { <https://semopenalex.org/work/W56779641> ?p ?o ?g. }
Showing items 1 to 72 of
72
with 100 items per page.
- W56779641 endingPage "4" @default.
- W56779641 startingPage "71" @default.
- W56779641 abstract "Chronic idiopathic intestinal pseudo-obstruction (CIPS) is a rare condition in which there is a defective motility of the gastrointestinal tract of unknown cause leading to repeated bouts of intestinal obstruction without organic explanation. This syndrome groups several ill-defined varieties of motor disorders that can sometimes be classified according to the presence of familial incidence and to the presence of muscular or nervous lesions. Nevertheless, a considerable proportion of cases cannot be ascribed to either type. CIPS is a very difficult challenge for pediatric surgeons because our role is never curative and because when we are involved in it is usually as a result of a false diagnosis. We present herein the experience of 2 Pediatric Surgery Departments in this entity. In the last 30 years we have been involved in the management of 16 children with CIPS. Male-to-female ratio was 5:11 and all but 3 patients had symptoms before 6 months of life. Thirteen had abdominal distension, 10 maldevelopment, 9 recurrent bouts of intestinal obstruction, 8 chronic diarrhea, 7 vomiting, 2 dysphagia and 2 constipation. Seven out of the 16 had urinary tract involvement and in three prenatal diagnosis of megacysts was made. The mean delayed time for diagnosis was 3.08 years. Esophageal or antroduodenal manometry was performed in 8 patients and it was abnormal in 7. Histologic and histochemical samples were available in 8 patients, but only in 4 was enough to make a diagnosis of myopathy. Twelve patients underwent 41 surgical procedures. Three are currently included in a program of home parenteral nutrition. Only three have died, and the mean age of the survivors is 13.9 years. In most of the patients with CIPS surgery is only useful for nutritional purposes, for diversion procedures or for intestinal transplantation in extreme cases. Every effort should be made to avoid unnecessary explorations, misdiagnosis and delay in the identification of the syndrome." @default.
- W56779641 created "2016-06-24" @default.
- W56779641 creator A5002796700 @default.
- W56779641 creator A5014177306 @default.
- W56779641 creator A5024969109 @default.
- W56779641 creator A5025357577 @default.
- W56779641 creator A5036142200 @default.
- W56779641 creator A5077581202 @default.
- W56779641 date "1999-04-01" @default.
- W56779641 modified "2023-10-17" @default.
- W56779641 title "[Diagnosis and therapeutic options in chronic idiopathic intestinal pseudo-obstruction: review of 16 cases]." @default.
- W56779641 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/10570859" @default.
- W56779641 hasPublicationYear "1999" @default.
- W56779641 type Work @default.
- W56779641 sameAs 56779641 @default.
- W56779641 citedByCount "2" @default.
- W56779641 crossrefType "journal-article" @default.
- W56779641 hasAuthorship W56779641A5002796700 @default.
- W56779641 hasAuthorship W56779641A5014177306 @default.
- W56779641 hasAuthorship W56779641A5024969109 @default.
- W56779641 hasAuthorship W56779641A5025357577 @default.
- W56779641 hasAuthorship W56779641A5036142200 @default.
- W56779641 hasAuthorship W56779641A5077581202 @default.
- W56779641 hasConcept C105702510 @default.
- W56779641 hasConcept C126322002 @default.
- W56779641 hasConcept C141071460 @default.
- W56779641 hasConcept C2776310010 @default.
- W56779641 hasConcept C2776356852 @default.
- W56779641 hasConcept C2779124032 @default.
- W56779641 hasConcept C2779787475 @default.
- W56779641 hasConcept C2780596822 @default.
- W56779641 hasConcept C2780852908 @default.
- W56779641 hasConcept C2780955771 @default.
- W56779641 hasConcept C2781112942 @default.
- W56779641 hasConcept C3017955636 @default.
- W56779641 hasConcept C71924100 @default.
- W56779641 hasConcept C90924648 @default.
- W56779641 hasConceptScore W56779641C105702510 @default.
- W56779641 hasConceptScore W56779641C126322002 @default.
- W56779641 hasConceptScore W56779641C141071460 @default.
- W56779641 hasConceptScore W56779641C2776310010 @default.
- W56779641 hasConceptScore W56779641C2776356852 @default.
- W56779641 hasConceptScore W56779641C2779124032 @default.
- W56779641 hasConceptScore W56779641C2779787475 @default.
- W56779641 hasConceptScore W56779641C2780596822 @default.
- W56779641 hasConceptScore W56779641C2780852908 @default.
- W56779641 hasConceptScore W56779641C2780955771 @default.
- W56779641 hasConceptScore W56779641C2781112942 @default.
- W56779641 hasConceptScore W56779641C3017955636 @default.
- W56779641 hasConceptScore W56779641C71924100 @default.
- W56779641 hasConceptScore W56779641C90924648 @default.
- W56779641 hasIssue "2" @default.
- W56779641 hasLocation W567796411 @default.
- W56779641 hasOpenAccess W56779641 @default.
- W56779641 hasPrimaryLocation W567796411 @default.
- W56779641 hasRelatedWork W1607201807 @default.
- W56779641 hasRelatedWork W1964805584 @default.
- W56779641 hasRelatedWork W1973270602 @default.
- W56779641 hasRelatedWork W1976447690 @default.
- W56779641 hasRelatedWork W2123430095 @default.
- W56779641 hasRelatedWork W2184798501 @default.
- W56779641 hasRelatedWork W2810401774 @default.
- W56779641 hasRelatedWork W4226049551 @default.
- W56779641 hasRelatedWork W56779641 @default.
- W56779641 hasRelatedWork W2187433924 @default.
- W56779641 hasVolume "12" @default.
- W56779641 isParatext "false" @default.
- W56779641 isRetracted "false" @default.
- W56779641 magId "56779641" @default.
- W56779641 workType "article" @default.