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- W58262446 abstract "症例は45歳の男性で,31歳時に小脳血管芽腫にて開頭腫瘍摘出術を施行した.家族歴にvon Hippel-Lindau病(以下,VHL病)はなかった.2007年5月の健診にて膵腫瘍を認め,精査加療目的7月上旬に当院紹介となった.精査にて非機能性膵内分泌腫瘍,膵漿液性嚢胞腫瘍の診断となり,8月下旬に幽門輪温存膵頭十二指腸切除術を施行された.病理では神経内分泌腫瘍,膵漿液性嚢胞腺腫の診断であった.本症例は家族歴のない散発性のVHL病であったため,小脳血管芽腫の手術の際には診断基準を満たさなかったが,14年経過した今回の手術でVHL病と診断された.家族歴がなくとも,網膜や中枢神経の血管芽腫などのVHL病を疑う疾患があれば,長期にわたるフォローが必要であると考えられた." @default.
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- W58262446 date "2010-01-01" @default.
- W58262446 modified "2023-10-01" @default.
- W58262446 title "A Case of von Hippel-Lindau Disease Diagnosed by the Occurrence of Pancreatic Endocrine Tumor" @default.
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- W58262446 doi "https://doi.org/10.5833/jjgs.43.179" @default.
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