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- W8599571 abstract "The prevalence of iron overload cardiomyopathy (IOC) is increasing. The spectrum of symptoms of IOC is varied. Early in the disease process, patients may be asymptomatic, whereas severely overloaded patients can have terminal heart failure complaints that are refractory to treatment. It has been shown that early recognition and intervention may alter outcomes. Biochemical markers and tissue biopsy, which have traditionally been used to diagnose and guide therapy, are not sensitive enough to detect early cardiac iron deposition. Newer diagnostic modalities such as magnetic resonance imaging are noninvasive and can assess quantitative cardiac iron load. Phlebotomy and chelating drugs are suboptimal means of treating IOC; hence, the roles of gene therapy, hepcidin, and calcium channel blockers are being actively investigated. There is a need for the development of clinical guidelines in order to improve the management of this emerging complex disease." @default.
- W8599571 created "2016-06-24" @default.
- W8599571 creator A5046340946 @default.
- W8599571 creator A5051632252 @default.
- W8599571 creator A5090769479 @default.
- W8599571 creator A5091772849 @default.
- W8599571 date "2010-09-01" @default.
- W8599571 modified "2023-10-13" @default.
- W8599571 title "Iron Overload Cardiomyopathy" @default.
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