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- W935127788 abstract "Publisher Summary This chapter discusses myasthenia gravis (MG) as the model antibody-mediated disease, and the newer neurologic diseases are also reviewed. MG is an acquired autoimmune disorder in which the postsynaptic AChRs are reduced in number or function, leading to muscle fatigue and weakness. The weakness often starts in the eye muscles, resulting in double vision and ptosis, but may involve any muscle group. MG is frequently associated with thymic abnormalities, so-called thymitis, in around 60% and thymoma in around 10% of patients. The division of MG into groups, depending on antibody status, thymic pathology, and age at onset, has been useful in defining the existence of different clinical subtypes that may result from different etiologies. Treatment includes anticholinesterases, nonspecific immunosuppression and, in appropriate younger patients, thymectomy. Despite much work in animal models of MG, no disease-specific immunosuppressive treatments are currently available. A new form of MG, associated with antibodies to MuSK, has been identified, and found to present some distinct clinical features." @default.
- W935127788 created "2016-06-24" @default.
- W935127788 creator A5006404326 @default.
- W935127788 creator A5062939642 @default.
- W935127788 date "2006-01-01" @default.
- W935127788 modified "2023-09-23" @default.
- W935127788 title "Myasthenia Gravis and other Antibody-Associated Neurological Diseases" @default.
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