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- W98996444 endingPage "169" @default.
- W98996444 startingPage "143" @default.
- W98996444 abstract "Combined immune deficiencies (CIDs) form a group of inherited immune disorders in which lymphocyte numbers may be diminished and lymphocyte functions are impaired. These disorders affect primarily T cells, typically disturbing their ability to provide assistance for antibody production and therefore causing decreased immunoglobulins. The disorders may also directly affect B cells and/or natural killer (NK) cells. The defects can occur during ontogeny and may be caused by genes that are known to cause severe combined immunodeficiency (SCID). In the case of CID, peripheral T cells are produced in greater numbers than in SCID due to less severe – i.e., hypomorphic – mutations that permit partial or full mature T cell egress from the thymus. Alternatively, defects in T cell function can occur at various stages of T cell receptor (TCR) signaling or cytokine responsiveness of mature T cells. Because B cells and NK cells have evolved similar signaling pathways, defects in these response mechanisms can impair B and/or NK cell functions." @default.
- W98996444 created "2016-06-24" @default.
- W98996444 creator A5014247790 @default.
- W98996444 creator A5071545468 @default.
- W98996444 date "2014-01-01" @default.
- W98996444 modified "2023-10-02" @default.
- W98996444 title "Combined Immune Deficiencies" @default.
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